LMPD Database

LMP004694

UniProt Annotations

Entry Information
Gene Nameprenyl (decaprenyl) diphosphate synthase, subunit 2
Protein EntryDLP1_HUMAN
UniProt IDQ86YH6
SpeciesHuman
Comments
Comment typeDescription
Alternative ProductsEvent=Alternative splicing; Named isoforms=2; Name=1; IsoId=Q86YH6-1; Sequence=Displayed; Name=2; IsoId=Q86YH6-2; Sequence=VSP_017098, VSP_017099;
Catalytic Activity(2E,6E)-farnesyl diphosphate + 7 isopentenyl diphosphate = 7 diphosphate + all-trans-decaprenyl diphosphate.
DiseaseCoenzyme Q10 deficiency, primary, 3 (COQ10D3) [MIM
FunctionSupplies decaprenyl diphosphate, the precursor for the side chain of the isoprenoid quinones ubiquinone-10.
PathwayCofactor biosynthesis; ubiquinone biosynthesis.
Sequence CautionSequence=AAH29491.1; Type=Frameshift; Positions=28; Evidence= ; Sequence=CAH73572.1; Type=Erroneous gene model prediction; Evidence= ; Sequence=CAI22355.1; Type=Erroneous gene model prediction; Evidence= ;
SimilarityBelongs to the FPP/GGPP synthase family.
Subcellular LocationMitochondrion .
SubunitHeterotetramer of 2 DPS1/TPRT and 2 DLP1 subunits.