LMPD Database

LMP002059

UniProt Annotations

Entry Information
Gene Namealpha-methylacyl-CoA racemase
Protein EntryAMACR_MOUSE
UniProt IDO09174
SpeciesMouse
Comments
Comment typeDescription
Catalytic Activity(2S)-2-methylacyl-CoA = (2R)-2-methylacyl-CoA.
FunctionRacemization of 2-methyl-branched fatty acid CoA esters. Responsible for the conversion of pristanoyl-CoA and C27-bile acyl-CoAs to their (S)-stereoisomers.
PathwayLipid metabolism; bile acid biosynthesis.
PathwayLipid metabolism; fatty acid metabolism.
Sequence CautionSequence=AAB72146.1; Type=Erroneous initiation; Note=Translation N-terminally extended.; Evidence={ECO:0000305};
SimilarityBelongs to the CaiB/BaiF CoA-transferase family. {ECO:0000305}.
Subcellular LocationPeroxisome {ECO:0000269|PubMed:10770938}. Mitochondrion {ECO:0000269|PubMed:10770938}.