LMPD Database

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LMP005481

Gene Information

Entrez Gene ID593
Gene Namebranched chain keto acid dehydrogenase E1, alpha polypeptide
Gene SymbolBCKDHA
SpeciesHomo sapiens
Gene Ontology (GO Annotations)
GO IDSourceTypeDescription
GO:0005947 IDA:HGNCCmitochondrial alpha-ketoglutarate dehydrogenase complex
GO:0005759 TAS:ReactomeCmitochondrial matrix
GO:0005739 IDA:UniProtCmitochondrion
GO:0003863 TAS:ProtIncF3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) activity
GO:0003826 IDA:HGNCFalpha-ketoacid dehydrogenase activity
GO:0016831 TAS:HGNCFcarboxy-lyase activity
GO:0046872 IEA:UniProtKB-KWFmetal ion binding
GO:0009083 IDA:HGNCPbranched-chain amino acid catabolic process
GO:0034641 TAS:ReactomePcellular nitrogen compound metabolic process
GO:0051591 IEA:EnsemblPresponse to cAMP
GO:0051384 IEA:EnsemblPresponse to glucocorticoid
GO:0007584 IEA:EnsemblPresponse to nutrient
GO:0044281 TAS:ReactomePsmall molecule metabolic process
BIOCYC Pathway Links
BIOCYC Pathway IDDescription
PWY-50462-oxoisovalerate decarboxylation to isobutanoyl-CoA
ILEUDEG-PWYisoleucine degradation I
REACTOME Pathway Links
REACTOME Pathway IDDescription
REACT_197Branched-chain amino acid catabolism