LMPD Database

LMP006028

Record overview

LMPD IDLMP006028
Gene ID201595
SpeciesHomo sapiens (Human)
Gene NameSTT3B, subunit of the oligosaccharyltransferase complex (catalytic)
Gene SymbolSTT3B
SynonymsCDG1X; SIMP; STT3-B
Alternate namesdolichyl-diphosphooligosaccharide--protein glycosyltransferase subunit STT3B; homolog of yeast STT3; oligosaccharyl transferase subunit STT3B; source of immunodominant MHC-associated peptides homolog; dolichyl-diphosphooligosaccharide protein glycotransferase; STT3, subunit of the oligosaccharyltransferase complex, homolog B
Chromosome3
Map Location3p23
EC Number2.4.99.18
SummaryThe protein encoded by this gene is a catalytic subunit of a protein complex that transfers oligosaccharides onto asparagine residues. Defects in this gene are a cause of congenital disorder of glycosylation Ix (CDG1X). [provided by RefSeq, Jun 2014]
OrthologsView orthologs and multiple alignments for STT3B

Proteins

dolichyl-diphosphooligosaccharide--protein glycosyltransferase subunit STT3B
Refseq ID:NP_849193
Protein GI:30578410
UniProt ID:Q8TCJ2
mRNA ID:NM_178862
Length:826
RefSeq Status:REVIEWED
MAEPSAPESKHKSSLNSSPWSGLMALGNSRHGHHGPGAQCAHKAAGGAAPPKPAPAGLSGGLSQPAGWQSLLSFTILFLAWLAGFSSRLFAVIRFESIIH
EFDPWFNYRSTHHLASHGFYEFLNWFDERAWYPLGRIVGGTVYPGLMITAGLIHWILNTLNITVHIRDVCVFLAPTFSGLTSISTFLLTRELWNQGAGLL
AACFIAIVPGYISRSVAGSFDNEGIAIFALQFTYYLWVKSVKTGSVFWTMCCCLSYFYMVSAWGGYVFIINLIPLHVFVLLLMQRYSKRVYIAYSTFYIV
GLILSMQIPFVGFQPIRTSEHMAAAGVFALLQAYAFLQYLRDRLTKQEFQTLFFLGVSLAAGAVFLSVIYLTYTGYIAPWSGRFYSLWDTGYAKIHIPII
ASVSEHQPTTWVSFFFDLHILVCTFPAGLWFCIKNINDERVFVALYAISAVYFAGVMVRLMLTLTPVVCMLSAIAFSNVFEHYLGDDMKRENPPVEDSSD
EDDKRNQGNLYDKAGKVRKHATEQEKTEEGLGPNIKSIVTMLMLMLLMMFAVHCTWVTSNAYSSPSVVLASYNHDGTRNILDDFREAYFWLRQNTDEHAR
VMSWWDYGYQIAGMANRTTLVDNNTWNNSHIALVGKAMSSNETAAYKIMRTLDVDYVLVIFGGVIGYSGDDINKFLWMVRIAEGEHPKDIRESDYFTPQG
EFRVDKAGSPTLLNCLMYKMSYYRFGEMQLDFRTPPGFDRTRNAEIGNKDIKFKHLEEAFTSEHWLVRIYKVKAPDNRETLDHKPRVTNIFPKQKYLSKK
TTKRKRGYIKNKLVFKKGKKISKKTV